Biventricular Arrhythmogenic Cardiomyopathy: a paradigmatic case
نویسندگان
چکیده
منابع مشابه
Atypical Clinical Presentation of Arrhythmogenic Biventricular Cardiomyopathy
Mailing Address: Inês Rangel • Serviço de Cardiologia, Centro Hospitalar de S. João. Alameda Professor Hernâni Monteiro. Postal Code 4200-319, Porto, Portugal. E-mail: [email protected] Manuscript received February 28, 2013; revised March 27, 2013; accepted April 23, 2013.
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Arrhythmogenic ventricular cardiomyopathy (AVC) is generally referred to as arrhythmogenic right ventricular (RV) cardiomyopathy/dysplasia and constitutes an inherited cardiomyopathy. Affected patients may succumb to sudden cardiac death (SCD), ventricular tachyarrhythmias (VTA) and heart failure. Genetic studies have identified causative mutations in genes encoding proteins of the intercalated...
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ژورنال
عنوان ژورنال: ScienceOpen Research
سال: 2015
ISSN: 2199-1006
DOI: 10.14293/s2199-1006.1.sor-med.azgtgz.v1